Item Type | Name |
Concept
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Mice, Inbred mdx
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Concept
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Mice, Knockout
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Concept
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Mice
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Concept
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Mice, Inbred C57BL
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Concept
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Mice, Transgenic
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Concept
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Mice, Mutant Strains
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Academic Article
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Hypoglossal neuropathology and respiratory activity in pompe mice.
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Academic Article
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Retrograde gene delivery to hypoglossal motoneurons using adeno-associated virus serotype 9.
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Academic Article
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Intrapleural administration of AAV9 improves neural and cardiorespiratory function in Pompe disease.
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Academic Article
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Sustained correction of motoneuron histopathology following intramuscular delivery of AAV in pompe mice.
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Academic Article
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Peripheral nerve and neuromuscular junction pathology in Pompe disease.
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Academic Article
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Stimulation of Respiratory Motor Output and Ventilation in a Murine Model of Pompe Disease by Ampakines.
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Academic Article
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Therapeutic rAAVrh10 Mediated SOD1 Silencing in Adult SOD1(G93A) Mice and Nonhuman Primates.
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Academic Article
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Power spectral analysis of hypoglossal nerve activity during intermittent hypoxia-induced long-term facilitation in mice.
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Academic Article
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Adeno-associated virus-delivered artificial microRNA extends survival and delays paralysis in an amyotrophic lateral sclerosis mouse model.
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Academic Article
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Neuropathology in respiratory-related motoneurons in young Pompe (Gaa(-/-)) mice.
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Academic Article
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Restrictive Lung Disease in the Cu/Zn Superoxide-Dismutase 1 G93A Amyotrophic Lateral Sclerosis Mouse Model.
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Academic Article
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Airway smooth muscle dysfunction in Pompe (Gaa-/- ) mice.
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Academic Article
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Systemic Delivery of AAVB1-GAA Clears Glycogen and Prolongs Survival in a Mouse Model of Pompe Disease.
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Academic Article
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Editing out five Serpina1 paralogs to create a mouse model of genetic emphysema.
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Academic Article
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AAV9 gene replacement therapy for respiratory insufficiency in very-long chain acyl-CoA dehydrogenase deficiency.
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Academic Article
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Comparisons of Infant and Adult Mice Reveal Age Effects for Liver Depot Gene Therapy in Pompe Disease.
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Academic Article
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Intralingual and Intrapleural AAV Gene Therapy Prolongs Survival in a SOD1 ALS Mouse Model.
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Academic Article
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The Respiratory Phenotype of Pompe Disease Mouse Models.
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Academic Article
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Intralingual Administration of AAVrh10-miRSOD1 Improves Respiratory But Not Swallowing Function in a Superoxide Dismutase-1 Mouse Model of Amyotrophic Lateral Sclerosis.
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Academic Article
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Motor axonopathies in a mouse model of Duchenne muscular dystrophy.
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Academic Article
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Respiratory pathology in the Optn-/- mouse model of Amyotrophic Lateral Sclerosis.
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Academic Article
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Corrigendum to "Respiratory pathology in the optn-/- mouse model of amyotrophic lateral sclerosis" [Respir. Physiol. Neurobiol. 282 (2020) 103525].
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Academic Article
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Genetic deletion of the Tas2r143/Tas2r135/Tas2r126 cluster reveals that TAS2Rs may not mediate bitter tastant-induced bronchodilation.
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Academic Article
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Adeno-Associated Virus-Mediated Gene Therapy in the Mashlool, Atp1a3Mashl/+, Mouse Model of Alternating Hemiplegia of Childhood.
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Academic Article
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Glycogen accumulation in smooth muscle of a Pompe disease mouse model.
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Academic Article
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Respiratory dysfunction in a mouse model of spinocerebellar ataxia type 7.
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Concept
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Mice, 129 Strain
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Academic Article
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What's new and what's next for gene therapy in Pompe disease?
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Academic Article
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Cross-species evolution of a highly potent AAV variant for therapeutic gene transfer and genome editing.
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Academic Article
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X-linked SBMA model mice display relevant non-neurological phenotypes and their expression of mutant androgen receptor protein in motor neurons is not required for neuromuscular disease.
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Academic Article
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Respiratory characterization of a humanized Duchenne muscular dystrophy mouse model.
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Academic Article
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Respiratory neuropathology in spinocerebellar ataxia type 7.
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Academic Article
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Respiratory pathology in the TDP-43 transgenic mouse model of amyotrophic lateral sclerosis.
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Academic Article
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Progressive central cardiorespiratory rate downregulation and intensifying epilepsy lead to sudden unexpected death in epilepsy in mouse model of the most common human ATP1A3 mutation.
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Academic Article
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Respiratory pathology in the mdx/utrn -/- mouse: A murine model for Duchenne Muscular Dystrophy (DMD).
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Academic Article
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GAA replacement improves respiratory muscle, neural, and alveolar pathology in the pompe mouse.
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Academic Article
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Neuromuscular junction transcriptome analysis of spinal and bulbar muscular atrophy mice implicates sarcomere gene expression and calcium flux dysregulation in disease pathogenesis.
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