Moyamoya Disease

"Moyamoya Disease" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus, MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure, which enables searching at various levels of specificity.

MeSH information

Definition | Details | More General Concepts | Related Concepts | More Specific Concepts

A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults.

Descriptor ID	D009072
MeSH Number(s)	C10.228.140.300.200.600 C10.228.140.300.510.200.737 C14.907.137.615 C14.907.253.123.620 C14.907.253.560.200.737
Concept/Terms	Moyamoya Disease Moyamoya Disease Progressive Intracranial Occlusive Arteropathy (Moyamoya) Moyamoya Syndrome Moya-Moya Disease Disease, Moya-Moya Moya Moya Disease Cerebrovascular Moyamoya Disease Moyamoya Disease, Primary Moyamoya Disease, Primary Disease, Primary Moyamoya Moyamoya Diseases, Primary Primary Moyamoya Disease Primary Moyamoya Diseases Moyamoya Disease, Classic Classic Moyamoya Disease Disease, Classic Moyamoya Moyamoya Disease, Secondary Moyamoya Disease, Secondary Secondary Moyamoya Disease

Below are MeSH descriptors whose meaning is more general than "Moyamoya Disease".

Diseases [C]
Nervous System Diseases [C10]
Central Nervous System Diseases [C10.228]
Brain Diseases [C10.228.140]
Cerebrovascular Disorders [C10.228.140.300]
Carotid Artery Diseases [C10.228.140.300.200]
Moyamoya Disease [C10.228.140.300.200.600]
Intracranial Arterial Diseases [C10.228.140.300.510]
Cerebral Arterial Diseases [C10.228.140.300.510.200]
Moyamoya Disease [C10.228.140.300.510.200.737]
Cardiovascular Diseases [C14]
Vascular Diseases [C14.907]
Arterial Occlusive Diseases [C14.907.137]
Moyamoya Disease [C14.907.137.615]
Cerebrovascular Disorders [C14.907.253]
Carotid Artery Diseases [C14.907.253.123]
Moyamoya Disease [C14.907.253.123.620]
Intracranial Arterial Diseases [C14.907.253.560]
Cerebral Arterial Diseases [C14.907.253.560.200]
Moyamoya Disease [C14.907.253.560.200.737]

Below are MeSH descriptors whose meaning is more specific than "Moyamoya Disease".

publications

Timeline | Most Recent

This graph shows the total number of publications written about "Moyamoya Disease" by people in this website by year, and whether "Moyamoya Disease" was a major or minor topic of these publications.

Bar chart showing 11 publications over 8 distinct years, with a maximum of 3 publications in 2016

To see the data from this visualization as text, click here.

Year	Major Topic	Minor Topic	Total
2009	1	0	1
2010	1	0	1
2016	1	2	3
2020	1	0	1
2021	1	0	1
2023	1	0	1
2024	2	0	2
2025	1	0	1

Below are the most recent publications written about "Moyamoya Disease" by people in Profiles.

Miller R, Anikpezie N, Hoffman H, Bako AT, Patel SD, Sahoo A, Aneni E, Wee CD, Albright KC, Latorre JGS, Liu JK, Agarwalla PK, Singla A, Khandelwal P, Otite FO. Demographic Disparities in the Incidence of Moyamoya Angiopathy in the United States. Neurology. 2025 Sep 09; 105(5):e214013.

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Suh L, Puri AS, Singh J, Kuhn AL. I saw the 'puff of smoke' sign before it vanished into thin air. Clin Imaging. 2024 Jul; 111:110190.

View in: PubMed
Kappel AD, Feroze AH, Torio E, Sukumaran M, Du R. Management of moyamoya disease: a review of current and future therapeutic strategies. J Neurosurg. 2024 Oct 01; 141(4):975-982.

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Youn DH, Kim N, Lee A, Han SW, Kim JT, Hong EP, Jung H, Jeong MS, Cho SM, Jeon JP. Autophagy and mitophagy-related extracellular mitochondrial dysfunction of cerebrospinal fluid cells in patients with hemorrhagic moyamoya disease. Sci Rep. 2023 08 23; 13(1):13753.

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Mathkour M, Werner C, Scullen T, Fennell VS, Nerva J, Amenta PS, Iwanaga J, Dumont AS, Bui CJ, Mortazavi MM, Hur MS, Tubbs RS. Detethering the superficial temporal artery: Application to tension free superficial temporal artery-middle cerebral artery bypasses. Clin Anat. 2022 May; 35(4):428-433.

View in: PubMed
Patel SD, Desai N, Rane S, Patel N, Desai R, Mehta T, Ollenschleger MD, Nanda A, Starke RM, Khandelwal P. Trends in hospitalizations and epidemiological characteristics of adults Moyamoya disorder in the United States. J Neurol Sci. 2020 Dec 15; 419:117165.

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Sekhar LN, Zeeshan Q, Natarajan SK. In Reply: Three-Vessel Anastomosis for Direct Bihemispheric Cerebral Revascularization. Oper Neurosurg. 2020 09 15; 19(4):E458-E460.

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Gaffar S, Eskander JP, Beakley BD, McClure BP, Amenta P, Pierre N. A case of central diabetes insipidus after ketamine infusion during an external to internal carotid artery bypass. J Clin Anesth. 2017 Feb; 36:72-75.

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Pricola Fehnel K, Duggins-Warf M, Zurakowski D, McKee-Proctor M, Majumder R, Raber M, Han X, Smith ER. Using urinary bFGF and TIMP3 levels to predict the presence of juvenile pilocytic astrocytoma and establish a distinct biomarker signature. J Neurosurg Pediatr. 2016 Oct; 18(4):396-407.

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Reynolds MR, Haydon DH, Caird J, Leonard JR. Radiation-Induced Moyamoya Syndrome after Proton Beam Therapy in the Pediatric Patient: A Case Series. Pediatr Neurosurg. 2016; 51(6):297-301.

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