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Lower limb areflexia without central and peripheral conduction abnormalities is highly suggestive of Gerstmann-Str?ussler-Scheinker disease Pro102Leu.

Salsano E, Fancellu R, Di Fede G, Ciano C, Scaioli V, Nanetti L, Politi LS, Tagliavini F, Mariotti C, Pareyson D. Lower limb areflexia without central and peripheral conduction abnormalities is highly suggestive of Gerstmann-Str?ussler-Scheinker disease Pro102Leu. J Neurol Sci. 2011 Mar 15; 302(1-2):85-8.

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