A group of congenital malformations involving the brainstem, cerebellum, upper spinal cord, and surrounding bony structures. Type II is the most common, and features compression of the medulla and cerebellar tonsils into the upper cervical spinal canal and an associated MENINGOMYELOCELE. Type I features similar, but less severe malformations and is without an associated meningomyelocele. Type III has the features of type II with an additional herniation of the entire cerebellum through the bony defect involving the foramen magnum, forming an ENCEPHALOCELE. Type IV is a form a cerebellar hypoplasia. Clinical manifestations of types I-III include TORTICOLLIS; opisthotonus; HEADACHE; VERTIGO; VOCAL CORD PARALYSIS; APNEA; NYSTAGMUS, CONGENITAL; swallowing difficulties; and ATAXIA. (From Menkes, Textbook of Child Neurology, 5th ed, p261; Davis, Textbook of Neuropathology, 2nd ed, pp236-46)

Descriptor ID	D001139
MeSH Number(s)	C10.500.680.291 C16.131.666.680.291
Concept/Terms	Arnold-Chiari Malformation Arnold-Chiari Malformation Arnold Chiari Malformation Malformation, Arnold-Chiari Malformation, Arnold Chiari Arnold-Chiari Deformity Arnold Chiari Deformity Deformity, Arnold-Chiari Arnold-Chiari Syndrome Arnold Chiari Syndrome Syndrome, Arnold-Chiari Arnold-Chiari Malformation, Type II Arnold-Chiari Malformation, Type II Arnold Chiari Malformation, Type II Chiari Malformation Type 2 Chiari Malformation Type II Arnold-Chiari Malformation, Type 2 Arnold Chiari Malformation, Type 2 Type II Arnold-Chiari Malformation Type II Arnold Chiari Malformation Arnold-Chiari Malformation, Type IV Arnold-Chiari Malformation, Type IV Arnold Chiari Malformation, Type IV Type IV Arnold-Chiari Malformation Type IV Arnold Chiari Malformation Arnold-Chiari Malformation, Type 4 Arnold Chiari Malformation, Type 4 Arnold-Chiari Malformation, Type I Arnold-Chiari Malformation, Type I Arnold Chiari Malformation, Type I Chiari Malformation Type I Type I Arnold-Chiari Malformation Type I Arnold Chiari Malformation Arnold-Chiari Malformation, Type 1 Arnold Chiari Malformation, Type 1 Arnold-Chiari Malformation, Type III Arnold-Chiari Malformation, Type III Arnold Chiari Malformation, Type III Type III Arnold-Chiari Malformation Type III Arnold Chiari Malformation Arnold-Chiari Malformation, Type 3 Arnold Chiari Malformation, Type 3

Below are MeSH descriptors whose meaning is more general than "Arnold-Chiari Malformation".

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Below are MeSH descriptors whose meaning is more specific than "Arnold-Chiari Malformation".